Pediatric Non-Functional Retroperitoneal Paragangilioma: A Rare Case Report

Author(s): Abdishakur Mohamed Abdi, Ismail Haki Gol, Abdullah yusuf Ali

Extra-adrenal paragangiliomas are uncommon neuroendocrine neoplasms with frequency 2-8 per million cases. They have an inclination to be malignant more than pheochromocytomas. Here we present a case of nonfunctional extra adrenal retroperitoneal paraganilioma occurring in 16-year-old male patient presented to with complaints of abdominal pain and heavens on the left hypochondria, CT scan revealed a retroperitoneal gross mass lesion measuring 114 × 99mm in the axial plane, extending from the upper quadrant level of the abdomen towards the inferior and containing necrotic areas in the central part. The mass was surgically removed successfully without intraoperative complications. Postoperative period was uneventful and patient discharged on day 7. Careful preoperative preparation and planning is mandatory as nature of tumor is endocrine tumor which secrete certain hormones and sudden rise or fall serum level of those hormones can result life threatening hypertension or hypotension. Full precaution must be taken to avoid these severe complications.